Uncommon cause of pelvic pain in adolescent female patient

Charalampos K. Plakias, Danae Makri, Sofia Papaioannou


A 13-year-old female patient presented to the emergency department with a 3-month recurrent and progressive pelvic pain during the menstrual bleeding. Her menarche was about 6 months ago. No abnormal findings were found on physical examination. The laboratory tests revealed normal white blood cell count. Pelvic ultrasound was initially performed (Fig.1), followed by magnetic resonance imaging (MRI) (Fig. 2). The patient then underwent a vaginohysteroscopy and a post-surgery MRI.


Keywords: Herlyn-Werner-Wunderlich syndrome, Renal agenesis, Mullerian duct, OHVIRA syndrome, pelvic MRI

Full Text:



Burgis J. Obstructive Müllerian anomalies: case report, diagnosis, and management. Am J Obstet Gynecol. 2001;185:338–344.

Del Vescovo R, Battisti S, Di Paola V, et al. Herlyn-werner-wunderlich syndrome: MRI findings, radiological guide (two cases and literature review), and differential diagnosis. BMC Med Imaging. 2012;12:4.

Lee JM, Lee JM. Herlyn-Werner-Wunderlich Syndrome: A Mini-review. Child Kidney Dis. 2018;22:12–16.

Candiani GB, Fedele L, Candiani M. Double uterus, blind hemivagina, and ipsilateral renal agenesis: 36 cases and long-term follow-up. Obstet Gynecol. 1997;90:26–32.

Orazi C, Lucchetti MC, Schingo PMS, et al. Herlyn-Werner-Wunderlich syndrome: uterus didelphys, blind hemivagina and ipsilateral renal agenesis. Sonographic and MR findings in 11 cases. Pediatr Radiol. 2007;37:657–665.

Gungor Ugurlucan F, Dural O, Yasa C, et al. Diagnosis, management, and outcome of obstructed hemivagina and ipsilateral renal agenesis (OHVIRA syndrome): Is there a correlation between MRI findings and outcome? Clin Imaging. 2020;59:172–178.

Aranke M, Nguyen KL, Wagner RD, et al. Haematometrocolpos and acute pelvic pain associated with cyclic uterine bleeding: OHVIRA syndrome. BMJ Case Rep [Internet]. 2018 [cited 2020 Oct 19];2018. Available from: https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5911096/.

DOI: http://dx.doi.org/10.36162/hjr.v7i1.427


  • There are currently no refbacks.